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Table of Contents > Abs + Ref
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Yonsei Med J. 2009 Jun;50(3):448-451.
Published online 2009 June 24.  doi: 10.3349/ymj.2009.50.3.448.
© Copyright: Yonsei University College of Medicine 2009
A Case of Catecholaminergic Polymorphic Ventricular Tachycardia
Seung-Yul Lee, Jin-Bae Kim, Eui Im, Woo-In Yang, Boyoung Joung, Moon-Hyoung Lee, and Sung-Soon Kim
Division of Cardiology, Yonsei Cardiovascular Center and Cardiovascular Research Institute, Yonsei Univercity College of Medicine, Seoul, Korea.

Corresponding author: Dr. Moon-Hyoung Lee, Division of Cardiology, Yonsei Cardiovascular Center and Cardiovascular Research Institute, Yonsei University College of Medicine, 250 Seongsan-ro, Seodaemun-gu, Seoul 120-752, Korea. Tel: 82-2-2228-8446, Fax: 82-2-393-2041, Email: mhlee@yuhs.ac
Received August 30, 2007; Revised October 17, 2007; Accepted October 17, 2007.

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted noncommercial use, distribution, and reproduction in any medium, provided the original work is properly cited.


Abstract

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a familial cardiac arrhythmia that is related to RYR2 or CASQ2 gene mutation. It occurs in patients with structurally normal heart and causes exercise-emotion-triggered syncope and sudden cardiac death. We experienced a case of CPVT in an 11 year-old female patient who was admitted for sudden cardiovascular collapse. The initial electrocardiogram (ECG) on emergency department revealed ventricular fibrillation. After multiple defibrillations, sinus rhythm was restored. However, recurrent ventricular fibrillation occurred during insertion of nasogastric tube without sedation in coronary care unit. On ECG monitoring, bidirectional ventricular tachycardia occurred with sinus tachycardia and then degenerated into ventricular fibrillation. To our knowledge, there has been no previous case report of CPVT triggered by sinus tachycardia in Korea. Therefore, we report the case as well as a review of the literature.

Keywords: Catecholamine, ventricular tachycardia.
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